con el diagnóstico histopatológico de cordoma de la base del cráneo .. magnética cerebral, corte sagital, secuencia T1, cordoma del clivus. Resección endoscópica de cordoma del clivus. Descripción de un chordoma; clivus; endoscopic resection; malignant tumor. RESUMEN. Download Citation on ResearchGate | On Dec 19, , Ines Gamboa and others published Resección endoscópica de cordoma del clivus. Descripción de un.

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Although this tumor lends itself to complete removal, long-term follow-up monitoring is needed to determine the possibility of recurrence. Also, proton-beam irradiation is reported cordoka be efficacious for the treatment of chordomas Increased T 2 -weighted MR signal relative to cerebrospinal fluid, which was present, has been described in some spinal and cranial chordomas with high mucoid content. British Journal of Cancer.

Intradural Retroclival Chordoma

Retrieved from ” https: Intradural extraosseous chordoma has clearly different features from those of typical chordoma It is uncommon, occurs almost exclusively in the prepontine and clival regions, and is encountered in 0. Under the impression of acoustic schwannoma, the patient underwent operation.

The radiological appearance of our tumor was not diagnosed either on plain radiography, Clkvus, or MR imaging.

A portion of the tumor with typical features of physaliphorous cells. Please review our privacy policy. Find articles by Yeon Soo Choo. Chordomas are ckivus radioresistant, requiring cordoja doses of coreoma to be controlled. Edit article Share article View revision history. Open in a separate window. Histological findings The tumor tissue was histologically characterized by lobules composed of typical physaliphorous cells with abundantly vacuolated cytoplasm. Wikimedia Commons has media related to Chordoma.


The patient was not aware of progressive neurological loss. Cranial nerve examination revealed no gag reflex, uvula deviation to left side, decreased hearing acuity on right ear, decreased taste on right side of tongue and numbness on right V1, V2 dermatome.

The solid, spherical, circumscribed tumor wall xel surrounded by delicate filamentous connective tissue and contained soft material that could be aspirated, as well as viscous fluid. It lay within the loose areolar tissue of Batson’s plexus and did not involve surrounding structures such as the common dural sac, nerve roots, vertebral body, or pedicle or ligamentous structures. Their illustration demonstrates a chondroid tumor-like nodule that differs histologically from cranial ecchordosis.

We report a case of a lumbar extraosseous extradural tumor with histological features of classic chordoma. The remainder of the neurological examination was clivuz normal ranges. National Center for Biotechnology InformationU.

As noted above germline duplication of brachyury has been identified as a major susceptibility mechanism in several chordoma families.

Intradural Retroclival Chordoma

The disc protrusion at the L-2 interspace was considered clinically significant in that it explained the presence of pain in the right thigh. This herniation was not evident on the magnetic resonance imaging despite axial sections through this interspace.

The Journal of Bone and Joint Surgery. Notochordal rests drl the true vertebrae are rare 2 and are primarily located centrally or posteriorly within vertebral bodies.

MRI of extensive clival chordoma in year-old male patient, axial view. Neuroradiology link – Pubmed citation. Electromicrographs of the tumor specimen. In contrast, radiosurgery has the advantage of high dose single-session irradiation and efficacy for small sized tumor mass 7 Since chordomas arise in bone, they are usually extradural and cordomz in local bone destruction.


They most commonly involve cervical particularly C2followed by lumbar, and then the thoracic spine. There are three histological variants of chordoma: Intradural chordomas are very rare tumors that should be distinguished from neurinomas and classic chordomas, because of their different biological behaviors.

Microneurosurgery of CNS Tumor; pp. There are currently no known environmental risk factors for chordoma. True malignant forms of cordoam occasionally have areas of typical chordoma as well as undifferentiated areas, most often fibrosarcoma.

Expert Recommendations for the Diagnosis and Treatment of Chordoma is a handbook produced by the Chordoma Foundation, which summarizes recommendations developed by a group of over 40 leading doctors who specialize in caring for chordoma patients.

The extradural tumor lay within the loose areolar tissue of Batson’s plexus, demonstrated no osseous involvement, and was completely removed. Although the histological, immunocytochemical, and ultrastructural features of this tumor are those of ordinary cranial, vertebral, or sacral chordoma, the tumor described in this report exhibits a different topography and growth pattern, being extraosseous and confined to the epidural space. Photomicrographs of the tumor specimen. Such tumors often showed extraosseous xlivus that were out of proportion to the degree of osseous involvement and were most often anterior and lateral but did involve the posterior spinal area.

Additionally, it represents an example of intraspinal extraosseous chordoma, a lesion not previously described. Fluid and gelatinous mucoid substance associated with recent and old hemorrhage and necrotic areas are found within these tumours.

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